Stargardt disease is an inherited disorder of the retina – the tissue at the back of the eye that senses light. The disease typically causes vision loss during childhood or adolescence, although in some forms, vision loss may not be noticed until later in adulthood. It is rare for people with the disease to become completely blind. For most people, vision loss progresses slowly over time to 20/200 or worse. (Normal vision is 20/20).
Stargardt disease is also called Stargardt macular dystrophy, juvenile macular degeneration (JMD), or fundus flavimaculatus. The disease causes progressive damage—or degeneration—of the macula, which is a small area in the center of the retina that is responsible for sharp, straight-ahead vision. Stargardt disease is one of several genetic disorders that cause Macular Degeneration. Experts estimate that 1 in 8-10 thousand people have Stargardt disease.